English Translation, Synonyms, Definitions and Usage Examples of Spanish Word ‘enfermedad de Degos’. Meanings of “enfermedad de degos” in English Spanish Dictionary: 1 result(s) Meanings of “enfermedad de degos” with other terms in English Spanish. Me llamo Loli tengo 37 años y vivo en Madrid y me diagnoticaron la enfermedad de Degos en despues de que perdiera la vision del ojo.
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Systemic manifestations are progressive and may lead to serious complications: Diagnostic methods Diagnosis is based primarily on the cutaneous clinical picture that is nearly pathognomonic.
Orphanet: Enfermedad de Degos
The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment. May Pages ee22 Pages From Monday to Friday from 9 a. Differential diagnosis The histology of early lesions resembles cutaneous lupus erythematosus see this term.
Ocular involvement, which affects the eyelids, conjuctiva, retina, sclera and the choroid plexus, as well as the development of diplopia and ophthalmoplegia as secondary side effects of the neurologic involvement dw, has also been described. The documents contained in this web site are presented for information purposes only.
As all patients may potentially develop the systemic, life-threatening variant, an annual follow-up is mandatory. If you are a member of the AEDV: Hypotheses implicating vasculitis, coagulopathy or a ebfermedad dysfunction of endothelial cells have been proposed. In the year has been indexed in the Medlinedatabase, and has become a vehicle for expressing the most current Spanish medicine and modern.
Later a wedge-shaped connective tissue necrosis in the deep dermis, due to a thrombotic occlusion of the small arteries and fnfermedad lymphocytes, occurs.
Summary and related texts. Summary Epidemiology Less than cases have been described in the literature.
Health care resources for this disease Expert centres 69 Diagnostic tests 0 Patient organisations 21 Orphan drug s 0. Pemphigus Vegetans in the Inguinal Folds. Check this box if you wish to receive a copy of your message. To improve our services and products, we use “cookies” own or third parties authorized to show advertising related to client preferences through the analyses of navigation customer behavior.
Clinical description MAP onset occurs in adults aged with skin lesions that appear initially as small erythematous papules, predominantly on the trunk and the upper extremities. Disease definition Malignant atrophic papulosis MAP is a rare, chronic, thrombo-obliterative vasculopathy characterized by papular skin lesions with central porcelain-white atrophy and a surrounding teleangiectatic rim. The etiopathogenesis of the disease remains unknown. Are you a health professional able to prescribe or dispense drugs?
Subscriber If you already have your login data, please click here. For all other comments, please send your remarks via contact us. Face, scalp, palms of hands and soles of feet are rarely involved.
Systemic lesions may affect the gastrointestinal tract and the central nervous system CNS and are potentially lethal.
Enfermedad de Degos
Prognosis Idiopathic, monosymptomatic, cutaneous presentations are benign, however, systemic manifestations can develop years after the occurrence of skin lesions.
No effective treatment for the systemic manifestations has been established, however, subcutaneous treprostinil has been dehos successfully in one case with intestinal and CNS manifestations. Continuing navigation will be considered as acceptance of this use. The histology of early lesions resembles cutaneous lupus erythematosus see this term. Over several days, the center of the lesions sinks and develops a characteristic enffermedad SJR uses a similar algorithm as the Google page rank; it provides a quantitative and qualitative measure of the journal’s impact.
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Therapeutic efforts with anticoagulants and compounds that facilitate blood perfusion, such as acetylosalicylic acid, pentoxifylline, dipyridamole, ticlodipine and heparin have achieved a partial regression of skin lesions in some individual cases.
Degoss onset occurs in adults aged with skin lesions that appear initially as small erythematous papules, predominantly on the trunk and the upper extremities.
enfermedad de degos
More developed lesions show prominent changes in the dermoepidermal junction, with atrophy of the epidermis and an area of sclerosis in the papillary dermis.
A clinical inspection of the skin should be combined with additional examinations including brain magnetic resonance tomography, gastroscopy, colonoscopy, X-ray of the chest and abdominal ultrasound, in order to assess the long-term prognosis. This item has received. It may more rarely manifest as pericarditis or in other organs such as the lungs, presenting as pleuritis. Many patients have been reported to have defects in blood coagulation.